深圳欣博盛生物科技有限公司 a1

ACADM Antibody
品牌:ProSci LLC
货号:25-092 规格:100 ul 目录价:¥9108.45
产品详情
* 以下信息仅供参考,详情请以原厂网站为准
产品名称:
ACADM Antibody
别名:
ACADM, ACAD1, MCAD, MCADH
反应种属:
Human
宿主来源:
Rabbit
实验应用:
ELISA,WB
克隆性:
Polyclonal
纯化方式:
Antibody is purified by peptide affinity chromatography method.
偶联:
Unconjugated
产品浓度:
batch dependent
保存温度:
For short periods of storage (days) store at 4˚C. For longer periods of storage, store ACADM antibody at -20˚C. As with any antibody avoid repeat freeze-thaw cycles.
运输温度:
Blue Ice
产品形式:
Liquid
存储溶液:
Purified antibody supplied in 1x PBS buffer with 0.09% (w/v) sodium azide and 2% sucrose.
产地:
美国
生产商:
Prosci
功能与背景:
ACADM Is the medium-chain specific (C4 to C12 straight chain) acyl-Coenzyme A dehydrogenase. The homotetramer enzyme catalyzes the initial step of the mitochondrial fatty acid beta-oxidation pathway. Clinical phenotypes are associated with ACADM hereditary deficiency.This gene encodes the medium-chain specific (C4 to C12 straight chain) acyl-Coenzyme A dehydrogenase. The homotetramer enzyme catalyzes the initial step of the mitochondrial fatty acid beta-oxidation pathway. Defects in this gene cause medium-chain acyl-CoA dehydrogenase deficiency, a disease characterized by hepatic dysfunction, fasting hypoglycemia, and encephalopathy, which can result in infantile death. Alternatively spliced transcript variants encoding different isoforms have been found for this gene.
Accession #:
NP_000007
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