深圳欣博盛生物科技有限公司 a1

BCKDHB Antibody
货号:F54271-0.08ML 规格:0.08 ml 目录价:¥2962.25
货号:F54271-0.4ML 规格:0.4 ml 目录价:¥6343.55
产品详情
* 以下信息仅供参考,详情请以原厂网站为准
产品名称:
BCKDHB Antibody
产品描述:
Branched-chain keto acid dehydrogenase is a multienzyme complex associated with the inner membrane of mitochondria, and functions in the catabolism of branched-chain amino acids. The complex consists of multiple copies of 3 components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). This gene encodes the E1 beta subunit, and mutations therein have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation, and feeding problems.
反应种属:
Human
宿主来源:
Rabbit
实验应用:
WB, IHC-P, IF, FACS
同种型:
Rabbit Ig
免疫原:
A portion of amino acids 41-70 from the human protein were used as the immunogen for the BCKDHB antibody.
克隆性:
Polyclonal (rabbit origin)
纯化方式:
Antigen affinity purified
保存温度:
Aliquot the BCKDHB antibody and store frozen at -20oC or colder. Avoid repeated freeze-thaw cycles.
产品形式:
Purified
存储溶液:
In 1X PBS, pH 7.4, with 0.09% sodium azide
产地:
美国
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