Glucosidase Alpha Acid Antibody / GAA-单抗-深圳欣博盛生物科技有限公司

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Glucosidase Alpha Acid Antibody / GAA

品牌：NSJ Bio

官网链接

说明书

折扣/货期

货号：RQ6025

规格：100 ug

目录价：￥6488.05

产品详情

* 以下信息仅供参考，详情请以原厂网站为准

产品名称:

Glucosidase Alpha Acid Antibody / GAA

产品描述:

Lysosomal alpha-glucosidase is an enzyme that in humans is encoded by the GAA gene. This gene encodes lysosomal alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. The encoded preproprotein is proteolytically processed to generate multiple intermediate forms and the mature form of the enzyme. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Alternative splicing results in multiple transcript variants.

反应种属:

Human

宿主来源:

Mouse

实验应用:

WB, IHC-P, IF

同种型:

Mouse IgG2b

免疫原:

Amino acids TALAWWEDMVAEFHDQVPFDGMWIDMNEPSNFIR from the human protein were used as the immunogen for the Glucosidase Alpha Acid antibody.

克隆性:

Monoclonal (mouse origin)

克隆号:

2G7

纯化方式:

Affinity purified

保存温度:

After reconstitution, the Glucosidase Alpha Acid antibody can be stored for up to one month at 4oC. For long-term, aliquot and store at -20oC. Avoid repeated freezing and thawing.

产品形式:

Purified

存储溶液:

0.5mg/ml if reconstituted with 0.2ml sterile DI water

产地:

美国

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