| 货号:GTX01944 | 规格:500μl | 目录价:¥10000 |
产品详情
* 以下信息仅供参考,详情请以原厂网站为准
产品名称:
gamma Sarcoglycan antibody [35DAG/21B5]
别名:
sarcoglycan gamma , 35DAG , A4 , DAGA4 , DMDA , DMDA1 , LGMD2C , LGMDR5 , MAM , SCARMD2 , SCG3 , gamma-SG
反应种属:
Human, Rabbit
宿主来源:
Mouse
实验应用:
IHC-Fr
同种型:
IgG2b
免疫原:
Synthetic peptide containing amino acids 167–178 of the rabbit gamma-sarcoglycan sequence (Noguchi et al., 1995).
克隆性:
Monoclonal
克隆号:
35DAG/21B5
纯化方式:
Unpurified
偶联:
Unconjugated
产品浓度:
保存温度:
Store as concentrated solution. Centrifuge briefly prior to opening vial. For short-term storage (1-2 weeks), store at 4ºC. For long-term storage, aliquot and store at -20ºC or below. Avoid multiple freeze-thaw cycles.
运输温度:
4°C
产品形式:
Liquid
存储溶液:
Tissue culture supernatant, 0.09% Sodium azide.
生产商:
GeneTex
功能与背景:
This gene encodes gamma-sarcoglycan, one of several sarcolemmal transmembrane glycoproteins that interact with dystrophin. The dystrophin-glycoprotein complex (DGC) spans the sarcolemma and is comprised of dystrophin, syntrophin, alpha- and beta-dystroglycans and sarcoglycans. The DGC provides a structural link between the subsarcolemmal cytoskeleton and the extracellular matrix of muscle cells. Defects in the encoded protein can lead to early onset autosomal recessive muscular dystrophy, in particular limb-girdle muscular dystrophy, type 2C (LGMD2C). [provided by RefSeq, Oct 2008]
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