Ataxin 1 antibody [2F5]-单抗-深圳欣博盛生物科技有限公司

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Ataxin 1 antibody [2F5]

品牌：GeneTex

官网链接

说明书

折扣/货期

货号：GTX80399

规格：100μl

目录价：￥5600

产品详情

* 以下信息仅供参考，详情请以原厂网站为准

产品名称:

Ataxin 1 antibody [2F5]

别名:

ataxin 1 , ATX1 , D6S504E , SCA1

反应种属:

Human

宿主来源:

Mouse

实验应用:

ELISA, FCM, ICC/IF, IHC-P, WB

同种型:

IgG1

免疫原:

Purified recombinant fragment of human ATXN1 expressed in E. Coli.

克隆性:

Monoclonal

克隆号:

2F5

纯化方式:

Unpurified

偶联:

Unconjugated

产品浓度:

保存温度:

Store as concentrated solution. Centrifuge briefly prior to opening vial. For short-term storage (1-2 weeks), store at 4ºC. For long-term storage, aliquot and store at -20ºC or below. Avoid multiple freeze-thaw cycles.

运输温度:

4°C

预期分子量:

产品形式:

Liquid

存储溶液:

Ascites, 0.03% Sodium azide.

生产商:

GeneTex

功能与背景:

The autosomal dominant cerebellar ataxias (ADCA) are a heterogeneous group of neurodegenerative disorders characterized by progressive degeneration of the cerebellum, brain stem and spinal cord. Clinically, ADCA has been divided into three groups: ADCA types I-III. ADCAI is genetically heterogeneous, with five genetic loci, designated spinocerebellar ataxia (SCA) 1, 2, 3, 4 and 6, being assigned to five different chromosomes. ADCAII, which always presents with retinal degeneration (SCA7), and ADCAIII often referred to as the `pure' cerebellar syndrome (SCA5), are most likely homogeneous disorders. Several SCA genes have been cloned and shown to contain CAG repeats in their coding regions. ADCA is caused by the expansion of the CAG repeats, producing an elongated polyglutamine tract in the corresponding protein. The expanded repeats are variable in size and unstable, usually increasing in size when transmitted to successive generations. The function of the ataxins is not known. This loc

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